Resumen El angiomiolipoma es una lesiĆ³n hamartomatosa, habitualmente de localizaciĆ³n renal asociado a esclerosis tuberosa. La ubicaciĆ³n nasosinusal es extremadamente infrecuente y se puede presentar con obstrucciĆ³n nasal y epistaxis. Se presentan dos casos de angiomiolipoma de cavidad nasal diagnosticados en el Hospital Carlos Van Buren de ValparaĆso. Ambos casos se presentaron como masa nasal unilateral, se estudiaron con tomografĆa computada y fueron tratados con biopsia escisional, sin presentar recidivas durante su seguimiento. El anigiomiolipoma estĆ” compuesto por vasos sanguĆneos, mĆŗsculo liso y adipocitos. Existen diferencias entre el angiomiolipoma del riĆ±Ć³n versus el de piel, cavidad oral y nasal (angiomiolipomas mucocutĆ”neos); estos Ćŗltimos son extremadamente infrecuentes, de menor tamaƱo, con presencia de agregados linfoides, negativos para antĆgeno especĆfico de melanoma HMB-45 y sin asociaciĆ³n a esclerosis tuberosa. Existen pocos casos reportados e n la literatura de esta patologĆa, por lo que existe poca evidencia. ClĆnicamente, se presentan con obstrucciĆ³n nasal, epistaxis recurrente, sensaciĆ³n de masa nasal. El estudio preoperatorio depende de su extensiĆ³n y puede incluir una tomografĆa computada y/o angiografĆa para identificar su irrigaciĆ³n. El diagnĆ³stico definitivo es anatomopatolĆ³gico. Si se logra la escisiĆ³n completa, no se han reportado recidivas, por lo que presenta un excelente pronĆ³stico.
Abstract Angiomyolipoma is a hamartomatous lesion, usually of a renal location associated with tuberous sclerosis. Nasosinusal location is extremely rare and can present with nasal obstruction and epistaxis. Two cases of angiomyolipoma of the nasal cavity diagnosed at the Carlos Van Buren Hospital in ValparaĆso are presented. Both cases presented as a unilateral nasal mass, and were studied with computed tomography, and treated with an excisional biopsy, with no recurrences during follow-up. Anigiomyolipoma is com posed of blood vessels, smooth muscle and adipocytes. There are differences between angiomyolipoma of the kidney versus skin, oral and nasal cavity (mucocutaneous angiomyolipomas). The latter are extremely infrequent, smaller in size, with the presence of lymphoid aggregates, negative for the HMB-45 specific melanoma antigen and without association with tuberous sclerosis. There are few cases reported in the literature of this pathology, so there is little evidence. Clinically, they present with nasal obstruction, recurrent epistaxis, sensation of nasal mass. The preoperative study depends on its extension and may include a computed tomography and/or angiography to identify its irrigation. The definitive diagnosis is pathological. If complete excision is achieved, no recurrences have been reported, so it has an excellent prognosis.
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